X-ray showed seven triphalangeal digits in right hand with corresponding metacarpals. On examination of function of hand the precise finger movements were absent and only crude grasp was evident. Movements at shoulder were grossly normal while that at the elbow and wrist were restricted in all range. Pre operative clinical and radiological status The forearm was short with evidence of scars of previous surgery ( Figure 1). She had seven digits in her right hand that were arranged symmetrically as mirror images on either side of a sagittal axis. She had underwent corrective osteotomy with ring fixator for correcting the wrist flexion and radial deviation three years prior to reporting to us for management of polydactyly. None of her siblings had any congenital disorders. She was the first child of non consanguineous parents with normal antenatal history. 3Ī 15 year old female patient presented with multiple fingers in her right hand with short forearm and radial deviation on flexion of the wrist. It falls under I2bv according to IFSSH 2 classification and type 1 in Al-Quattan classification. 1 There are a few case reports of this rare anomaly. The preaxial ulna is often hypoplastic and supports the duplicated carpal elements. There is duplication of ulna and absence of radius.
The thumb is absent despite presence of seven digits. In most cases there is mirrored symmetry with a central digit and 3 digits on either side representing the middle ring and small fingers. Mirror hand or ulnar dimelia is a very rare congenital anomaly characterized by symmetric duplication of the upper limb in the midline.
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